Anti-GCDH Polyclonal Antibody,BR

英文名称： Anti-GCDH Polyclonal Antibody
中文名称： 戊二酰辅酶A脱氢酶抗体
规格： 100ul ; 50ul
宿主： Rabbit
克隆类型： Polyclonal Antibody
亚型： IgG
交叉反应： Rat ; Mouse ; Human
应用： WB ; IHC-P ; ELISA
稀释比例： WB 1:200-2000. IHC-P 1:50-200.

靶标： GCDH
别名： ACAD5,EC 1.3.99.7,GCD,Gcdh,GCDH_HUMAN,Glutaryl CoA dehydrogenase,Glutaryl CoA dehydrogenase,mitochondrial,Glutaryl Coenzyme A dehydrogenase,Glutaryl-CoA dehydrogenase,mitochondrial,MS781,
背景说明： The protein encoded by this gene belongs to the acyl-CoA dehydrogenase family. It catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and CO(2) in the degradative pathway of L-lysine, L-hydroxylysine, and L-tryptophan metabolism. It uses electron transfer flavoprotein as its electron acceptor. The enzyme exists in the mitochondrial matrix as a homotetramer of 45-kD subunits. Mutations in this gene result in the metabolic disorder glutaric aciduria type 1, which is also known as glutaric acidemia type I. Alternative splicing of this gene results in multiple transcript variants. A related pseudogene has been identified on chromosome 12.
Swiss Prot： Q92947
Gene ID： 2639
亚细胞定位： Mitochondrion
研究领域： 新陈代谢
免疫原： Recombinant protein of human GCDHPublic Immunogen Range 149-438aa
理论分子量： 48kDa

纯化方法： Affinity purification
储存液： PBS with 0.02% sodium azide，50% glycerol，pH7.3.
储存条件： Store at -20℃. Avoid freeze/thaw cycles.
运输条件： 冷冻运输

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